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產(chǎn)品規(guī)格
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BN40986R-100ul
100ul
¥2360.00
交叉反應(yīng):Mouse,Rat(predicted:Human,Cow) 推薦應(yīng)用:WB,IHC-P,IHC-F,ELISA
BN40986R-200ul
200ul
¥3490.00
交叉反應(yīng):Mouse,Rat(predicted:Human,Cow) 推薦應(yīng)用:WB,IHC-P,IHC-F,ELISA
產(chǎn)品描述
英文名稱 | GALT |
中文名稱 | 磷酸半乳糖尿苷酸轉(zhuǎn)移酶1抗體 |
別 名 | Gal 1 P uridylyltransferase; Galactose 1 phosphate uridyl transferase; Galactose 1 phosphate uridylyltransferase; UDP glucose hexose 1 phosphate uridylyltransferase; GALT_HUMAN. |
研究領(lǐng)域 | 腫瘤 細胞生物 免疫學(xué) 激酶和磷酸酶 |
抗體來源 | Rabbit |
克隆類型 | Polyclonal |
交叉反應(yīng) | Mouse, Rat, (predicted: Human, Cow, ) |
產(chǎn)品應(yīng)用 | WB=1:500-2000 ELISA=1:5000-10000 IHC-P=1:100-500 IHC-F=1:100-500 (石蠟切片需做抗原修復(fù)) not yet tested in other applications. optimal dilutions/concentrations should be determined by the end user. |
分 子 量 | 43kDa |
細胞定位 | 細胞漿 |
性 狀 | Liquid |
濃 度 | 1mg/ml |
免 疫 原 | KLH conjugated synthetic peptide derived from human GALT:251-350/379 |
亞 型 | IgG |
純化方法 | affinity purified by Protein A |
儲 存 液 | 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. |
保存條件 | Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. |
PubMed | PubMed |
產(chǎn)品介紹 | GALT (Galactose 1 phosphate uridyl transferase) catalyzes the second step of the Leloir pathway of galactose metabolism, namely the conversion of UDP glucose + galactose 1 phosphate to glucose 1 phosphate + UDP galactose. The absence of this enzyme results in classic galactosemia in humans and can be fatal in the newborn period if lactose is not removed from the diet. The pathophysiology of galactosemia has not been clearly defined. Subunit: Homodimer (Probable). DISEASE: Defects in GALT are the cause of galactosemia (GALCT) [MIM:230400]. Galactosemia is an inherited disorder of galactose metabolism that causes jaundice, cataracts, and mental retardation. Similarity: Belongs to the galactose-1-phosphate uridylyltransferase type 1 family. SWISS: P07902 Gene ID: 2592 Database links: Entrez Gene: 2592 Human Entrez Gene: 14430 Mouse Omim: 606999 Human SwissProt: P07902 Human SwissProt: Q03249 Mouse Unigene: 522090 Human Unigene: 439669 Mouse Unigene: 102781 Rat Important Note: This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
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